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Syringomyelia presenting with unilateral optic neuropathy: a case report

Purpose: In this case report, we present two cases of syringomyelia with optic neuropathy. Findings: In Case 1, a 36-year-old Malay lady presented to our clinic with acute onset of blurring of vision in her left eye that she experienced since past 1 month. She was diagnosed with syringomyelia 12...

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Main Authors:	Ngoo, Qi Zhe, Tai, Evelyn Li Min, Wan Hitam, Wan Hazabbah
Format:	Article
Language:	English
Published:	Dove Medical Press 2017
Subjects:	RE Ophthalmology
Online Access:	http://eprints.usm.my/37241/1/%28Syringomyelia_presenting_with_unilateral%29_IMCRJ-129239-031417.pdf http://eprints.usm.my/37241/ https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5359140/
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spelling	my.usm.eprints.37241 http://eprints.usm.my/37241/ Syringomyelia presenting with unilateral optic neuropathy: a case report Ngoo, Qi Zhe Tai, Evelyn Li Min Wan Hitam, Wan Hazabbah RE Ophthalmology Purpose: In this case report, we present two cases of syringomyelia with optic neuropathy. Findings: In Case 1, a 36-year-old Malay lady presented to our clinic with acute onset of blurring of vision in her left eye that she experienced since past 1 month. She was diagnosed with syringomyelia 12 years ago and was on conservative management. Her visual acuity was 6/6 in the right eye and counting fingers at 1 m in the left. There was a positive relative afferent pupillary defect in her left eye. Optic nerve functions of her left eye were reduced. Visual field showed a left inferior field defect. Her extraocular muscle movements were full. Magnetic resonance imaging of the brain and spine showed syringomyelia at the level of C2–C6 and T2–T9. Both of her optic nerves were normal. Her condition improved with intravenous and oral corticosteroids. In Case 2, a 44-year-old Malay lady presented to our clinic with a progressive central scotoma in her right eye that she experienced since past 1 month. She had previous history of recurrent episodes of weakness in both of her lower limbs from past 8 months. Visual acuity in her right and left eye was 6/9 and 6/6, respectively. The relative afferent pupillary defect in her right eye was positive. Optic nerve functions of her right eye were affected. Visual field showed a central scotoma in her right eye. Her extraocular muscle movements were full. Fundoscopy of her right eye showed a pale optic disc. Her left eye fundus was normal. Magnetic resonance imaging of the brain and spine showed syringomyelia at T3–T6. Both of her optic nerves were normal. A diagnosis of syringomyelia with right optic atrophy was performed. Her condition improved with intravenous and oral corticosteroids. Conclusion: Optic neuropathy is a rare neuro-ophthalmic manifestation in patients with syringomyelia. Prompt diagnosis and timely management are essential to avoid a poor visual outcome. Intravenous corticosteroids are beneficial in the treatment of early optic neuropathy in syringomyelia. Dove Medical Press 2017 Article PeerReviewed application/pdf en http://eprints.usm.my/37241/1/%28Syringomyelia_presenting_with_unilateral%29_IMCRJ-129239-031417.pdf Ngoo, Qi Zhe and Tai, Evelyn Li Min and Wan Hitam, Wan Hazabbah (2017) Syringomyelia presenting with unilateral optic neuropathy: a case report. International Medical Case Reports Journal, 10. pp. 87-91. ISSN 1179-142X https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5359140/
institution	Universiti Sains Malaysia
building	Hamzah Sendut Library
collection	Institutional Repository
continent	Asia
country	Malaysia
content_provider	Universiti Sains Malaysia
content_source	USM Institutional Repository
url_provider	http://eprints.usm.my/
language	English
topic	RE Ophthalmology
spellingShingle	RE Ophthalmology Ngoo, Qi Zhe Tai, Evelyn Li Min Wan Hitam, Wan Hazabbah Syringomyelia presenting with unilateral optic neuropathy: a case report
description	Purpose: In this case report, we present two cases of syringomyelia with optic neuropathy. Findings: In Case 1, a 36-year-old Malay lady presented to our clinic with acute onset of blurring of vision in her left eye that she experienced since past 1 month. She was diagnosed with syringomyelia 12 years ago and was on conservative management. Her visual acuity was 6/6 in the right eye and counting fingers at 1 m in the left. There was a positive relative afferent pupillary defect in her left eye. Optic nerve functions of her left eye were reduced. Visual field showed a left inferior field defect. Her extraocular muscle movements were full. Magnetic resonance imaging of the brain and spine showed syringomyelia at the level of C2–C6 and T2–T9. Both of her optic nerves were normal. Her condition improved with intravenous and oral corticosteroids. In Case 2, a 44-year-old Malay lady presented to our clinic with a progressive central scotoma in her right eye that she experienced since past 1 month. She had previous history of recurrent episodes of weakness in both of her lower limbs from past 8 months. Visual acuity in her right and left eye was 6/9 and 6/6, respectively. The relative afferent pupillary defect in her right eye was positive. Optic nerve functions of her right eye were affected. Visual field showed a central scotoma in her right eye. Her extraocular muscle movements were full. Fundoscopy of her right eye showed a pale optic disc. Her left eye fundus was normal. Magnetic resonance imaging of the brain and spine showed syringomyelia at T3–T6. Both of her optic nerves were normal. A diagnosis of syringomyelia with right optic atrophy was performed. Her condition improved with intravenous and oral corticosteroids. Conclusion: Optic neuropathy is a rare neuro-ophthalmic manifestation in patients with syringomyelia. Prompt diagnosis and timely management are essential to avoid a poor visual outcome. Intravenous corticosteroids are beneficial in the treatment of early optic neuropathy in syringomyelia.
format	Article
author	Ngoo, Qi Zhe Tai, Evelyn Li Min Wan Hitam, Wan Hazabbah
author_facet	Ngoo, Qi Zhe Tai, Evelyn Li Min Wan Hitam, Wan Hazabbah
author_sort	Ngoo, Qi Zhe
title	Syringomyelia presenting with unilateral optic neuropathy: a case report
title_short	Syringomyelia presenting with unilateral optic neuropathy: a case report
title_full	Syringomyelia presenting with unilateral optic neuropathy: a case report
title_fullStr	Syringomyelia presenting with unilateral optic neuropathy: a case report
title_full_unstemmed	Syringomyelia presenting with unilateral optic neuropathy: a case report
title_sort	syringomyelia presenting with unilateral optic neuropathy: a case report
publisher	Dove Medical Press
publishDate	2017
url	http://eprints.usm.my/37241/1/%28Syringomyelia_presenting_with_unilateral%29_IMCRJ-129239-031417.pdf http://eprints.usm.my/37241/ https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5359140/
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score	13.211869

Syringomyelia presenting with unilateral optic neuropathy: a case report

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