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A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report

Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal prolife...

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Main Authors: How, Soon Hin, Sa'at@Yusof, Azlin, Pang, Yong-Kek, Liam, Chong-Kin
Format: Article
Language:English
Published: University of Malaya Medical Centre 2006
Subjects:
R Medicine (General)
Online Access:http://irep.iium.edu.my/44330/1/case_of_lymphangioleiomyomatosis.pdf
http://irep.iium.edu.my/44330/
http://jummec.um.edu.my/filebank/published_article/3326/How%20SH.pdf
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spelling my.iium.irep.443302015-08-21T01:40:20Z http://irep.iium.edu.my/44330/ A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report How, Soon Hin Sa'at@Yusof, Azlin Pang, Yong-Kek Liam, Chong-Kin R Medicine (General) Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal proliferation of smooth muscle-like cells that grow over a course of time to obstruct airways, lymphatic and blood vessels. We report a case of LAM in a young woman who presented with a spontaneous pneumothorax. Computed tomography scan of the thorax and abdomen showed homogenous thin-walled cystic lesions with normal intervening lung parenchyma and multiple lesions in her kidneys with Hounsfield units similar to that of fat. University of Malaya Medical Centre 2006 Article REM application/pdf en http://irep.iium.edu.my/44330/1/case_of_lymphangioleiomyomatosis.pdf How, Soon Hin and Sa'at@Yusof, Azlin and Pang, Yong-Kek and Liam, Chong-Kin (2006) A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report. Journal of Health and Translational Medicine, 6 (2). pp. 35-38. ISSN 2289-392X (O), 1823-7339 (P) http://jummec.um.edu.my/filebank/published_article/3326/How%20SH.pdf
institution Universiti Islam Antarabangsa Malaysia
building IIUM Library
collection Institutional Repository
continent Asia
country Malaysia
content_provider International Islamic University Malaysia
content_source IIUM Repository (IREP)
url_provider http://irep.iium.edu.my/
language English
topic R Medicine (General)
spellingShingle R Medicine (General)
How, Soon Hin
Sa'at@Yusof, Azlin
Pang, Yong-Kek
Liam, Chong-Kin
A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report
description Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal proliferation of smooth muscle-like cells that grow over a course of time to obstruct airways, lymphatic and blood vessels. We report a case of LAM in a young woman who presented with a spontaneous pneumothorax. Computed tomography scan of the thorax and abdomen showed homogenous thin-walled cystic lesions with normal intervening lung parenchyma and multiple lesions in her kidneys with Hounsfield units similar to that of fat.
format Article
author How, Soon Hin
Sa'at@Yusof, Azlin
Pang, Yong-Kek
Liam, Chong-Kin
author_facet How, Soon Hin
Sa'at@Yusof, Azlin
Pang, Yong-Kek
Liam, Chong-Kin
author_sort How, Soon Hin
title A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report
title_short A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report
title_full A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report
title_fullStr A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report
title_full_unstemmed A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report
title_sort case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report
publisher University of Malaya Medical Centre
publishDate 2006
url http://irep.iium.edu.my/44330/1/case_of_lymphangioleiomyomatosis.pdf
http://irep.iium.edu.my/44330/
http://jummec.um.edu.my/filebank/published_article/3326/How%20SH.pdf
_version_ 1643612555884625920
score 13.211869

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